https://doi.org/10.4081/itjm.2023.1595

Adult-onset Still’s disease with secondary macrophage activation syndrome: a case report

Vol. 17 No. 1 (2023)
Published: 29 May 2023
adult-onset Still’s disease, secondary macrophage activation syndrome
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Authors

Giuseppe Nicoletti
giuseppenicoletti2266@gmail.com
https://orcid.org/0009-0009-4479-1426
Internal Medicine, Madonna delle Grazie Hospital, Matera, Italy.
Antonio Bonelli
Internal Medicine, Madonna delle Grazie Hospital, Matera, Italy.
Rocco Clemente
Internal Medicine, Madonna delle Grazie Hospital, Matera, Italy.
Simona Ciuffreda
Internal Medicine, Madonna delle Grazie Hospital, Matera, Italy.
Gaetano Dentamaro
Internal Medicine, Madonna delle Grazie Hospital, Matera, Italy.
Agata Tiziana La Masa
Internal Medicine, Madonna delle Grazie Hospital, Matera, Italy.
Vito Lascaro
Internal Medicine, Madonna delle Grazie Hospital, Matera, Italy.
Pasquale Santarcangelo
Internal Medicine, Madonna delle Grazie Hospital, Matera, Italy.

We describe a case of adult-onset Still’s disease (AOSD) with secondary macrophage activation syndrome. AOSD is a rare disease with unknown origin. Rarely it’s complicated by secondary macrophage activation syndrome, which is a life-threatening disorder. Because the diagnosis of AOSD is essential for exclusion and complications are life-threatening, it is mandatory for a prompt and extensive diagnostic workup and treatment.

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Giuseppe Nicoletti, Internal Medicine, Madonna delle Grazie Hospital, Matera

Internal Medicine director

Antonio Bonelli, Internal Medicine, Madonna delle Grazie Hospital, Matera

MD

Rocco Clemente, Internal Medicine, Madonna delle Grazie Hospital, Matera

MD

Simona Ciuffreda, Internal Medicine, Madonna delle Grazie Hospital, Matera

MD

Gaetano Dentamaro, Internal Medicine, Madonna delle Grazie Hospital, Matera

MD

Agata Tiziana La Masa, Internal Medicine, Madonna delle Grazie Hospital, Matera

MD

Vito Lascaro, Internal Medicine, Madonna delle Grazie Hospital, Matera

MD

Pasquale Santarcangelo, Internal Medicine, Madonna delle Grazie Hospital, Matera

MD

How to Cite

Nicoletti, G., Bonelli, A., Clemente, R., Ciuffreda, S., Dentamaro, G., La Masa, A. T., Lascaro, V., & Santarcangelo, P. (2023). Adult-onset Still’s disease with secondary macrophage activation syndrome: a case report. Italian Journal of Medicine, 17(1). https://doi.org/10.4081/itjm.2023.1595
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